The inner part of the ear contains tiny hair cells (nerve endings), that change sounds into electric signals. The nerves then carry these signals to the brain.
Sensorineural hearing loss (SNHL) is caused by damage to these special cells, or to the nerve fibers in the inner ear. Sometimes, the hearing loss is caused by damage to the nerve that carries the signals to the brain.
Sensorineural deafness that is present at birth (congenital) is most often due to:
Sign language (for those with severe hearing loss)
Speech reading (such as lip reading and using visual cues to aid communication)
A cochlear implant may be recommended for certain people with very severe hearing loss. Surgery is done to place the implant. The implant makes sounds seem louder, but does not restore normal hearing.
You will also learn strategies for living with hearing loss and advice to share with those around you for talking to someone with hearing loss.
Hildebrand MS, Husein M, Smith RJH. Genetic sensorineural hearing loss. In: Cummings CW, Flint PW, Haughey BH, et al, eds. Otolaryngology: Head & Neck Surgery. 5th ed. Philadelphia, Pa: Mosby Elsevier; 2010:chap 147.
Arts HA. Sensorineural hearing loss in adults. In: Cummings CW, Flint PW, Haughey BH, et al, eds. Otolaryngology: Head & Neck Surgery. 5th ed. Philadelphia, Pa: Mosby Elsevier;2010:chap 149.
Noise-Induced Hearing Loss. National Institute on Deafness and Other Communication Disorders. NIH Pub. No. 97-4233. Updated: October 2008.
Chau JK, Lin, JRJ, Atashband, S, Irvine, RA, Westerberg, BD. Systematic review of the evidence for the etiology of adult sensorineural hearing loss. The Laryngoscope. 2010, Vol 120(5): 1011-1021.
Luc Jasmin, MD, PhD, FRCS (C), FACS, Department of Neurosurgery at Cedars-Sinai Medical Center, Los Angeles CA; Department of Surgery at Los Robles Hospital, Thousand Oaks CA; Department of Surgery at Ashland Community Hospital, Ashland OR; Department of Surgery at Cheyenne Regional Medical Center, Cheyenne WY; Department of Anatomy at UCSF, San Francisco CA. Review provided by VeriMed Healthcare Network. Also reviewed by David Zieve, MD, MHA, Bethanne Black, and the A.D.A.M. Editorial team.